Surgical treatment of congenital heart disease with Eisenmenger syndrome

Ulugbek Mazhidov 1, Rakhima Mekenbayeva 1 * , Yerbol Aldabergenov 1
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1 Pediatric Cardiac Surgery Department, National Scientific Medical Center, Nur-Sultan city, Republic of Kazakhstan
* Corresponding Author
J CLIN MED KAZ, Volume 18, Issue 1, pp. 14-18.
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Article provides review of the available world literature on performing surgical correction of the atrioventricular septal defect (AVSD) in patients with Eisenmenger syndrome such as: basic pathophysiological principles, technique, indications, clinical and hemodynamic results. Currently, according to the literature, there is no clarity in the choice of a method for correcting severe congenital heart defects in combination with Eisenmenger syndrome (one - or two-step approach). The article presents the results of studies of both one-and two-stage approaches to correction of  the atrioventricular septal defect (AVSD) in this category of patients with their advantages and disadvantages.


Mazhidov U, Mekenbayeva R, Aldabergenov Y. Surgical treatment of congenital heart disease with Eisenmenger syndrome. J CLIN MED KAZ. 2021;18(1):14-8.


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